Aplasia Cutis Congenita of the Scalp with a Familial Pattern: A Case Report
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Abstract:
Aplasia Cutis Conginita (ACC) is a condition characterized by congenital absence of skin, usually on the scalp. ACC can occur as an isolated condition or in the presence of other congenital anomalies. Here we describe a case of a 16 days old baby girl with an isolated ACC of the scalp. Her elder two siblings have been diagnosed with ACC with concomitant cardiac or limb anomalies. The patient was managed conservatively until the defect has scarred 6 months later.
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aplasia cutis congenita of the scalp with a familial pattern: a case report
aplasia cutis conginita (acc) is a condition characterized by congenital absence of skin, usually on the scalp. acc can occur as an isolated condition or in the presence of other congenital anomalies. here we describe a case of a 16 days old baby girl with an isolated acc of the scalp. her elder two siblings have been diagnosed with acc with concomitant cardiac or limb anomalies. the patient wa...
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full textAplasia cutis congenita: a case report.
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full textAplasia Cutis Congenita of the Scalp
Dr. João Paulo Cavalcante de Almeida – Rua Paulo Morais 130 60175-175 Fortaleza CE Brasil. E-mail: [email protected] Aplasia cutis congenita (ACC) is an uncommon disorder that presents as a focal defect of the skin at birth, frequently involving the midline over the skull vertex (70%), but it may affect any region of the body. Since 1767, about 500 cases have been reported in medica...
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Journal title
volume 5 issue None
pages 298- 302
publication date 2016-07
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